Annotation Detail

Information
Associated Genes
ADAMTS13
Associated Variants
ADAMTS13 p.Arg1060Trp (p.R1060W) ( ENST00000355699.7, ENST00000356589.6, ENST00000371916.5, ENST00000371929.7 )
ADAMTS13 p.Arg1123Cys (p.R1123C) ( ENST00000355699.7, ENST00000356589.6, ENST00000371916.5, ENST00000371929.7 )
ADAMTS13 p.Arg1219Trp (p.R1219W) ( ENST00000355699.7, ENST00000356589.6, ENST00000371910.1, ENST00000371916.5, ENST00000371929.7 )
ADAMTS13 p.Arg1060Trp (p.R1060W) ( ENST00000355699.7, ENST00000356589.6, ENST00000371916.5, ENST00000371929.7 )
ADAMTS13 p.Arg1123Cys (p.R1123C) ( ENST00000355699.7, ENST00000356589.6, ENST00000371916.5, ENST00000371929.7 )
ADAMTS13 p.Arg1219Trp (p.R1219W) ( ENST00000355699.7, ENST00000356589.6, ENST00000371910.1, ENST00000371916.5, ENST00000371929.7 )
Associated Disease
Congenital Thrombotic Thrombocytopenic Purpura
Source Database
DisGeNET
Description
We investigated the spectrum of ADAMTS13 gene mutations in patients with TTP and congenital ADAMTS13 deficiency to establish the consequences on ADAMTS13 processing and activity.
Pubmed
17003922
Original source reporting the Gene Disease association
UNIPROT
DisGENET score for the Gene Disease association
0.453224706861814
Year of publication
2006
Drugs