Annotation Detail

Information
Associated Genes
TBX1
Associated Variants
NF1 p.Arg1241Ter (p.R1241*) ( ENST00000691014.1, ENST00000356175.7, ENST00000358273.9, ENST00000696138.1 )
NF1 p.Arg1241Ter (p.R1241*) ( ENST00000356175.7, ENST00000358273.9, ENST00000691014.1, ENST00000696138.1 )
Associated Disease
neurofibromatosis 1
Source Database
DisGeNET
Description
Three members of a Portuguese family, who exhibited clinical evidence of neurofibromatosis type 1 (NF1), were found to possess different heritable and pathological mutations in their NF1 genes: a 1.5-Mb deletion spanning the entire NF1 gene, a truncating CGA-->TGA transition in exon 22 (R1241X), and a frameshift mutation in exon 29 (5406insT).
Pubmed
12483293
Original source reporting the Gene Disease association
BeFree
DisGENET score for the Gene Disease association
0.000271441872080303
Year of publication
2003
Drugs