Annotation Detail

Information
Associated Genes
PLEC
Associated Variants
PLEC p.Arg3139Ter (p.R3139*) ( ENST00000322810.8, ENST00000345136.8, ENST00000354589.7, ENST00000354958.6, ENST00000356346.7, ENST00000357649.6, ENST00000527096.5, ENST00000527303.2, ENST00000398774.6, ENST00000436759.6, ENST00000528025.6, ENST00000685198.1, ENST00000687971.1, ENST00000693060.1 )
PLEC p.Arg3139Gly (p.R3139G) ( ENST00000322810.8, ENST00000345136.8, ENST00000354589.7, ENST00000354958.6, ENST00000356346.7, ENST00000357649.6, ENST00000398774.6, ENST00000436759.6, ENST00000527096.5, ENST00000527303.2, ENST00000528025.6, ENST00000685198.1, ENST00000687971.1, ENST00000693060.1 )
PLEC p.Gln415Ter (p.Q415*) ( ENST00000322810.8, ENST00000345136.8, ENST00000354589.7, ENST00000354958.6, ENST00000356346.7, ENST00000357649.6, ENST00000398774.6, ENST00000436759.6, ENST00000527096.5, ENST00000527303.2, ENST00000528025.6, ENST00000685198.1, ENST00000687971.1, ENST00000693060.1 )
PLEC p.Arg3139Ter (p.R3139*) ( ENST00000322810.8, ENST00000345136.8, ENST00000354589.7, ENST00000354958.6, ENST00000356346.7, ENST00000357649.6, ENST00000398774.6, ENST00000436759.6, ENST00000527096.5, ENST00000687971.1, ENST00000693060.1, ENST00000527303.2, ENST00000528025.6, ENST00000685198.1 )
PLEC p.Arg3139Gly (p.R3139G) ( ENST00000322810.8, ENST00000345136.8, ENST00000354589.7, ENST00000354958.6, ENST00000356346.7, ENST00000357649.6, ENST00000398774.6, ENST00000436759.6, ENST00000527096.5, ENST00000527303.2, ENST00000528025.6, ENST00000685198.1, ENST00000687971.1, ENST00000693060.1 )
PLEC p.Gln415Ter (p.Q415*) ( ENST00000322810.8, ENST00000345136.8, ENST00000354589.7, ENST00000354958.6, ENST00000356346.7, ENST00000357649.6, ENST00000398774.6, ENST00000436759.6, ENST00000527096.5, ENST00000527303.2, ENST00000528025.6, ENST00000685198.1, ENST00000687971.1, ENST00000693060.1 )
Associated Disease
Epidermolysis Bullosa Simplex With Pyloric Atresia
Source Database
DisGeNET
Description
NA
Original source reporting the Gene Disease association
CLINVAR
DisGENET score for the Gene Disease association
0.360814325616241
Year of publication
NA
Drugs