Annotation Detail

Information
Associated Genes
BSCL2
Associated Variants
HNRNPUL2-BSCL2 c.*512C>T, BSCL2 p.Ser154Leu (p.S154L) ( ENST00000683296.1, ENST00000407022.7, ENST00000684475.1, ENST00000682223.1, ENST00000421906.5, ENST00000405837.5, ENST00000403734.2, ENST00000278893.11, ENST00000449636.6, ENST00000684067.1, ENST00000360796.10, ENST00000679883.1, ENST00000524862.6, ENST00000403550.5 )
HNRNPUL2-BSCL2 c.*512C>T, BSCL2 p.Ser154Leu (p.S154L) ( ENST00000278893.11, ENST00000360796.10, ENST00000403550.5, ENST00000405837.5, ENST00000407022.7, ENST00000421906.5, ENST00000449636.6, ENST00000524862.6, ENST00000679883.1, ENST00000682223.1, ENST00000683296.1, ENST00000684067.1, ENST00000684475.1, ENST00000403734.2 )
Associated Disease
Spastic paraplegia 17
Source Database
DisGeNET
Description
We studied the first Korean families with clinical features resembling classic Silver syndrome and dHMN type V. Direct sequencing analysis of the BSCL2 gene revealed a Ser90Leu mutation in the proband, a younger sister, and one of two sons of the proband.
Pubmed
17486577
Original source reporting the Gene Disease association
BeFree
DisGENET score for the Gene Disease association
0.365352892571485
Year of publication
2007
Drugs