Annotation Detail

Information
Associated Genes
ERCC4
Associated Variants
ERCC4 p.Arg153His (p.R153H) ( ENST00000682617.1, ENST00000575156.5, ENST00000311895.8 )
ERCC4 p.Arg153Pro (p.R153P) ( ENST00000311895.8, ENST00000575156.5, ENST00000682617.1 )
ERCC4 p.Arg799Trp (p.R799W) ( ENST00000311895.8, ENST00000682617.1 )
ERCC4 p.Arg153His (p.R153H) ( ENST00000311895.8, ENST00000575156.5, ENST00000682617.1 )
ERCC4 p.Arg153Pro (p.R153P) ( ENST00000311895.8, ENST00000575156.5, ENST00000682617.1 )
ERCC4 p.Arg799Trp (p.R799W) ( ENST00000311895.8, ENST00000682617.1 )
Associated Disease
progeria
Source Database
DisGeNET
Description
In an attempt to determine how mutations in XPF can lead to such diverse symptoms, the effects of a progeria-causing mutation (XPF(R153P)) were compared to an XP-causing mutation (XPF(R799W)) in vitro and in vivo.
Pubmed
20221251
Original source reporting the Gene Disease association
BeFree
DisGENET score for the Gene Disease association
0.00081432561624091
Year of publication
2010
Drugs