Annotation Detail

Information
Associated Genes
SOD1
Associated Variants
SOD1 p.His47Arg (p.H47R) ( ENST00000270142.11, ENST00000389995.4 )
SOD1 p.His47Arg (p.H47R) ( ENST00000270142.11, ENST00000389995.4 )
Associated Disease
AMYOTROPHIC LATERAL SCLEROSIS 1
Source Database
DisGeNET
Description
Human familial amyotrophic lateral sclerosis with an H46R mutant Cu/Zn superoxide dismutase (SOD1) gene is characterized by initial muscle weakness and atrophy in the legs and a very long-term clinical course (approximately 15 years).
Pubmed
17549011
Original source reporting the Gene Disease association
BeFree
DisGENET score for the Gene Disease association
0.52
Year of publication
2007
Drugs