Annotation Detail

Information
Associated Genes
SOD1
Associated Variants
SOD1 p.Ile113Thr (p.I113T) ( ENST00000270142.11, ENST00000389995.4 )
SOD1 p.Ile114Thr (p.I114T) ( ENST00000270142.11, ENST00000389995.4 )
SOD1 p.Ile113Thr (p.I113T) ( ENST00000270142.11, ENST00000389995.4 )
SOD1 p.Ile114Thr (p.I114T) ( ENST00000270142.11, ENST00000389995.4 )
Associated Disease
amyotrophic lateral sclerosis
Source Database
DisGeNET
Description
A patient is described with a 20 year duration of motor neuron disease, with clinical features of ALS, who was heterozygous for a point mutation ATT to ACT leading to substitution of isoleucine for threonine at codon 113 in exon 4 of SOD-1.
Pubmed
7673954
Original source reporting the Gene Disease association
BeFree
DisGENET score for the Gene Disease association
0.437872511657633
Year of publication
1995
Drugs