Annotation Detail

Information
Associated Genes
SOD1
Associated Variants
SOD1 p.Gly13Arg (p.G13R) ( ENST00000270142.11, ENST00000389995.4 )
SOD1 p.Gly42Ser (p.G42S) ( ENST00000270142.11, ENST00000389995.4 )
SOD1 p.Asp91Ala (p.D91A) ( ENST00000270142.11, ENST00000389995.4 )
SOD1 p.Gly13Arg (p.G13R) ( ENST00000270142.11, ENST00000389995.4 )
SOD1 p.Gly42Ser (p.G42S) ( ENST00000270142.11, ENST00000389995.4 )
SOD1 p.Asp91Ala (p.D91A) ( ENST00000270142.11, ENST00000389995.4 )
Associated Disease
Progressive cGVHD
Source Database
DisGeNET
Description
In 7 out of 39 FALS patients we found the following SOD1 gene mutations: i) a new G12R missense mutation in exon 1, found in a patient with a slowly progressive disease course; ii) the G41S mutation, in four unrelated patients with rapidly progressive course complicated with cognitive decline in two of them; iii) the L114F mutation, in a patient with a slowly progressive phenotype; iv) the D90A mutation, in a heterozygous patient with atypical phenotype.
Pubmed
15789135
Original source reporting the Gene Disease association
BeFree
DisGENET score for the Gene Disease association
0.00081432561624091
Year of publication
2005
Drugs