Annotation Detail

Information
Associated Genes
NLRP3
Associated Variants
NLRP3 p.Asp303Asn (p.D303N) ( ENST00000336119.8, ENST00000474792.2, ENST00000391827.3, ENST00000348069.7, ENST00000366496.7, ENST00000391828.8, ENST00000643234.2, ENST00000697350.1, ENST00000697408.2 )
NLRP3 p.Asp303His (p.D303H) ( ENST00000474792.2, ENST00000391827.3, ENST00000391828.8, ENST00000336119.8, ENST00000348069.7, ENST00000366496.7, ENST00000643234.2, ENST00000697350.1, ENST00000697408.2 )
NLRP3 p.Asp303Asn (p.D303N) ( ENST00000336119.8, ENST00000348069.7, ENST00000366496.7, ENST00000391827.3, ENST00000391828.8, ENST00000474792.2, ENST00000643234.2, ENST00000697350.1, ENST00000697408.2 )
NLRP3 p.Asp303His (p.D303H) ( ENST00000336119.8, ENST00000348069.7, ENST00000366496.7, ENST00000391827.3, ENST00000391828.8, ENST00000474792.2, ENST00000643234.2, ENST00000697350.1, ENST00000697408.2 )
Associated Disease
Chronic Infantile Neurological, Cutaneous, and Articular Syndrome
Source Database
DisGeNET
Description
Our findings identify the novel p.D303H NLRP3 variant in a Spanish patient with CINCA/NOMID as a new disease-causing mutation, which was detected as a somatic, nongermline mutation in hematopoietic and nonhematopoietic cell lineages.
Pubmed
20131270
Original source reporting the Gene Disease association
BeFree
DisGENET score for the Gene Disease association
0.450043349266971
Year of publication
2010
Drugs