Annotation Detail

Information
Associated Genes
GAA
Associated Variants
GAA p.Lys903del (p.K903del) ( ENST00000390015.7, ENST00000570803.6, ENST00000714062.1, ENST00000714057.1, ENST00000714054.1, ENST00000577106.6, ENST00000714058.1, ENST00000302262.8, ENST00000714055.1 )
GAA p.Lys903del (p.K903del) ( ENST00000302262.8, ENST00000390015.7, ENST00000570803.6, ENST00000577106.6, ENST00000714054.1, ENST00000714055.1, ENST00000714057.1, ENST00000714058.1, ENST00000714062.1 )
GAA p.Leu299Pro (p.L299P) ( ENST00000302262.8, ENST00000714055.1, ENST00000714058.1, ENST00000390015.7, ENST00000570803.6, ENST00000714062.1, ENST00000714057.1, ENST00000577106.6, ENST00000714054.1 )
GAA p.Leu299Arg (p.L299R) ( ENST00000714054.1, ENST00000577106.6, ENST00000714057.1, ENST00000714062.1, ENST00000390015.7, ENST00000570803.6, ENST00000714058.1, ENST00000302262.8, ENST00000714055.1 )
GAA p.Met318Thr (p.M318T) ( ENST00000714062.1, ENST00000570803.6, ENST00000390015.7, ENST00000714054.1, ENST00000577106.6, ENST00000714057.1, ENST00000714058.1, ENST00000302262.8, ENST00000714055.1 )
GAA p.Glu521Lys (p.E521K) ( ENST00000570803.6, ENST00000714058.1, ENST00000302262.8, ENST00000714055.1, ENST00000714062.1, ENST00000390015.7, ENST00000714054.1, ENST00000577106.6, ENST00000714057.1 )
GAA p.Asp645Glu (p.D645E) ( ENST00000714055.1, ENST00000302262.8, ENST00000714058.1, ENST00000714062.1, ENST00000390015.7, ENST00000570803.6, ENST00000577106.6, ENST00000714054.1, ENST00000714057.1 )
GAA p.Asp645= (p.D645=) ( ENST00000714057.1, ENST00000714054.1, ENST00000577106.6, ENST00000390015.7, ENST00000570803.6, ENST00000714062.1, ENST00000714058.1, ENST00000714055.1, ENST00000302262.8 )
GAA p.Leu299Pro (p.L299P) ( ENST00000302262.8, ENST00000390015.7, ENST00000570803.6, ENST00000577106.6, ENST00000714054.1, ENST00000714055.1, ENST00000714057.1, ENST00000714058.1, ENST00000714062.1 )
GAA p.Leu299Arg (p.L299R) ( ENST00000302262.8, ENST00000390015.7, ENST00000570803.6, ENST00000577106.6, ENST00000714054.1, ENST00000714055.1, ENST00000714057.1, ENST00000714058.1, ENST00000714062.1 )
GAA p.Met318Thr (p.M318T) ( ENST00000302262.8, ENST00000390015.7, ENST00000570803.6, ENST00000577106.6, ENST00000714054.1, ENST00000714055.1, ENST00000714057.1, ENST00000714058.1, ENST00000714062.1 )
GAA p.Glu521Lys (p.E521K) ( ENST00000302262.8, ENST00000390015.7, ENST00000570803.6, ENST00000577106.6, ENST00000714054.1, ENST00000714055.1, ENST00000714057.1, ENST00000714058.1, ENST00000714062.1 )
GAA p.Asp645Glu (p.D645E) ( ENST00000302262.8, ENST00000390015.7, ENST00000570803.6, ENST00000577106.6, ENST00000714054.1, ENST00000714055.1, ENST00000714057.1, ENST00000714058.1, ENST00000714062.1 )
GAA p.Asp645= (p.D645=) ( ENST00000302262.8, ENST00000390015.7, ENST00000570803.6, ENST00000577106.6, ENST00000714054.1, ENST00000714055.1, ENST00000714057.1, ENST00000714058.1, ENST00000714062.1 )
Associated Disease
Glycogen storage disease type II, infantile
Source Database
DisGeNET
Description
NA
Original source reporting the Gene Disease association
CLINVAR
DisGENET score for the Gene Disease association
0.12
Year of publication
NA
Drugs