Annotation Detail

Information
Associated Genes
HNF1A
Associated Variants
HNF1A p.Ile27Leu (p.I27L) ( ENST00000541395.5, ENST00000257555.11, ENST00000400024.6, ENST00000544413.2 )
HNF1A p.Pro224Ser (p.P224S) ( ENST00000257555.11, ENST00000400024.6, ENST00000544413.2, ENST00000541395.5 )
HNF1A p.Ile27Leu (p.I27L) ( ENST00000257555.11, ENST00000400024.6, ENST00000541395.5, ENST00000544413.2 )
HNF1A p.Pro224Ser (p.P224S) ( ENST00000257555.11, ENST00000400024.6, ENST00000541395.5, ENST00000544413.2 )
Associated Disease
Maturity onset diabetes mellitus in young
Source Database
DisGeNET
Description
A new mutation in the hepatocyte nuclear factor-1-alpha gene (P224S) in a newly discovered German family with maturity-onset diabetes of the young 3 (MODY 3). Family members carry additionally the homozygous I27L amino acid polymorphism in the HNF1 alpha gene.
Pubmed
15031772
Original source reporting the Gene Disease association
BeFree
DisGENET score for the Gene Disease association
0.0290442803125925
Year of publication
2004
Drugs