Annotation Detail

Information
Associated Genes
POLG
Associated Variants
POLG p.Tyr955Cys (p.Y955C) ( ENST00000636937.2, ENST00000268124.11, ENST00000442287.6 )
POLG p.Tyr955Cys (p.Y955C) ( ENST00000268124.11, ENST00000442287.6, ENST00000636937.2 )
Associated Disease
chronic progressive external ophthalmoplegia
Source Database
DisGeNET
Description
The Y955C substitution in POLG leads to autosomal dominant progressive external ophthalmoplegia (PEO) with other severe phenotypes.
Pubmed
17725985
Original source reporting the Gene Disease association
BeFree
DisGENET score for the Gene Disease association
0.158406294920018
Year of publication
2007
Drugs