Annotation Detail

Information
Associated Genes
POLG
Associated Variants
POLG p.Glu1143Gly (p.E1143G) ( ENST00000442287.6, ENST00000636937.2, ENST00000268124.11 )
POLG p.Trp748Ser (p.W748S) ( ENST00000442287.6, ENST00000636937.2, ENST00000268124.11 )
POLG p.Glu1143Gly (p.E1143G) ( ENST00000268124.11, ENST00000442287.6, ENST00000636937.2 )
POLG p.Trp748Ser (p.W748S) ( ENST00000268124.11, ENST00000442287.6, ENST00000636937.2 )
Associated Disease
Ataxia
Source Database
DisGeNET
Description
In humans, POLGalpha W748S in cis with an E1143G mutation has been linked to a new type of recessive ataxia, MIRAS, which is the most common inherited ataxia in Finland.
Pubmed
20153822
Original source reporting the Gene Disease association
BeFree
DisGENET score for the Gene Disease association
0.00652453645159142
Year of publication
2010
Drugs