Annotation Detail

Information
Associated Genes
POLG
Associated Variants
POLG p.Trp748Ser (p.W748S) ( ENST00000442287.6, ENST00000636937.2, ENST00000268124.11 )
POLG p.Trp748Ser (p.W748S) ( ENST00000268124.11, ENST00000442287.6, ENST00000636937.2 )
Associated Disease
Diffuse Cerebral Sclerosis of Schilder
Source Database
DisGeNET
Description
Homozygous W748S mutation in the POLG1 gene in patients with juvenile-onset Alpers syndrome and status epilepticus.
Pubmed
18294203
Original source reporting the Gene Disease association
BeFree
DisGENET score for the Gene Disease association
0.139507596006318
Year of publication
2008
Drugs