Annotation Detail

Information
Associated Genes
POLG
Associated Variants
POLG p.Pro587Leu (p.P587L) ( ENST00000442287.6, ENST00000636937.2, ENST00000268124.11 )
POLG p.Pro587Leu (p.P587L) ( ENST00000268124.11, ENST00000442287.6, ENST00000636937.2 )
Associated Disease
Leukoencephalopathies
Source Database
DisGeNET
Description
We report a recessive family with features of MNGIE but no leukoencephalopathy in which two patients carry three missense mutations in POLG, of which two are novel mutations (N846S and P587L).
Pubmed
12825077
Original source reporting the Gene Disease association
BeFree
DisGENET score for the Gene Disease association
0.000542883744160607
Year of publication
2003
Drugs