Annotation Detail

Information
Associated Genes
POLG
Associated Variants
POLG p.Ala467Thr (p.A467T) ( ENST00000268124.11, ENST00000636937.2, ENST00000442287.6 )
POLG p.Ala467Thr (p.A467T) ( ENST00000268124.11, ENST00000442287.6, ENST00000636937.2 )
Associated Disease
Alpers Syndrome (disorder)
Source Database
DisGeNET
Description
Proof of progression over time: finally fulminant brain, muscle, and liver affection in Alpers syndrome associated with the A467T POLG1 mutation.
Pubmed
18783964
Original source reporting the Gene Disease association
BeFree
DisGENET score for the Gene Disease association
0.48868613990657
Year of publication
2009
Drugs