Annotation Detail

Information
Associated Genes
POLG
Associated Variants
POLG p.Ala467Thr (p.A467T) ( ENST00000268124.11, ENST00000636937.2, ENST00000442287.6 )
POLG p.Ala467Thr (p.A467T) ( ENST00000268124.11, ENST00000442287.6, ENST00000636937.2 )
Associated Disease
PROGRESSIVE EXTERNAL OPHTHALMOPLEGIA WITH MITOCHONDRIAL DNA DELETIONS, AUTOSOMAL RECESSIVE
Source Database
DisGeNET
Description
Mutation of POLG is associated with progressive external ophthalmoplegia characterized by mtDNA deletions.
Pubmed
11431686
Original source reporting the Gene Disease association
UNIPROT
DisGENET score for the Gene Disease association
0.480542883744161
Year of publication
2001
Drugs