Annotation Detail

Information
Associated Genes
POLG
Associated Variants
POLG p.Ala467Thr (p.A467T) ( ENST00000268124.11, ENST00000636937.2, ENST00000442287.6 )
POLG p.Ala467Thr (p.A467T) ( ENST00000268124.11, ENST00000442287.6, ENST00000636937.2 )
Associated Disease
Alpers Syndrome (disorder)
Source Database
DisGeNET
Description
We describe a 3.5-year-old female with Alpers disease with a POLG genotype of p.A467T/p.G848S and with a lethal outcome.
Pubmed
19766516
Original source reporting the Gene Disease association
BeFree
DisGENET score for the Gene Disease association
0.48868613990657
Year of publication
2010
Drugs