Annotation Detail

Information
Associated Genes
MECP2
Associated Variants
MECP2 p.Ala455Thr (p.A455T) ( ENST00000415944.4, ENST00000303391.11, ENST00000453960.7, ENST00000628176.2 )
MECP2 p.Ala455Thr (p.A455T) ( ENST00000303391.11, ENST00000415944.4, ENST00000453960.7, ENST00000628176.2 )
Associated Disease
MECP2-related disorder
Source Database
ClinVar
Description
NM_001110792.2(MECP2):c.1363G>A (p.Ala455Thr) AND MECP2-related disorder
ClinVar Allele ID
45153
ClinVar RefSeq Alternation Syntax
NM_001316337.2:c.1048G>A
ClinVar RefSeq Alternation Syntax
NM_001369392.2:c.1048G>A
ClinVar RefSeq Alternation Syntax
NM_001110792.2:c.1363G>A
ClinVar RefSeq Alternation Syntax
NM_001386139.1:c.658G>A
ClinVar RefSeq Alternation Syntax
NM_001369391.2:c.1048G>A
ClinVar RefSeq Alternation Syntax
NM_001386137.1:c.658G>A
ClinVar RefSeq Alternation Syntax
NM_001386138.1:c.658G>A
ClinVar RefSeq Alternation Syntax
NM_001369394.2:c.1048G>A
ClinVar RefSeq Alternation Syntax
NM_004992.4:c.1327G>A
ClinVar RefSeq Alternation Syntax
NM_001369393.2:c.1048G>A
Clinical Significance Description
Likely benign
Clinical Significance Last Update
2022-08-07
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV004541028
ClinVar Disease
MECP2-related disorder
Observed Origin Sample
germline
Drugs