Annotation Detail

Information
Associated Genes
TRPM4
Associated Variants
TRPM4 p.Glu7Lys (p.E7K) ( ENST00000252826.10, ENST00000427978.6, ENST00000599628.5 )
TRPM4 p.Glu7Lys (p.E7K) ( ENST00000252826.10, ENST00000427978.6, ENST00000599628.5 )
Associated Disease
TRPM4-related disorder
Source Database
ClinVar
Description
NM_017636.4(TRPM4):c.19G>A (p.Glu7Lys) AND TRPM4-related disorder
ClinVar Allele ID
18809
ClinVar RefSeq Alternation Syntax
NM_001321285.2:c.-311G>A
ClinVar RefSeq Alternation Syntax
NM_001321283.2:c.-148G>A
ClinVar RefSeq Alternation Syntax
NM_001321282.2:c.-1354G>A
ClinVar RefSeq Alternation Syntax
NM_001195227.2:c.19G>A
ClinVar RefSeq Alternation Syntax
NM_001321281.2:c.19G>A
ClinVar RefSeq Alternation Syntax
NM_017636.4:c.19G>A
Clinical Significance Description
Likely pathogenic
Clinical Significance Last Update
2023-07-13
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV004532279
ClinVar Disease
TRPM4-related disorder
Observed Origin Sample
germline
Drugs