Annotation Detail

Information
Associated Genes
ABCA4
Associated Variants
ABCA4 p.Arg2030Gln (p.R2030Q) ( ENST00000370225.4 )
ABCA4 p.Arg2030Gln (p.R2030Q) ( ENST00000370225.4 )
Associated Disease
ABCA4-related disorder
Source Database
ClinVar
Description
NM_000350.3(ABCA4):c.6089G>A (p.Arg2030Gln) AND ABCA4-related disorder
ClinVar Allele ID
105317
ClinVar RefSeq Alternation Syntax
NM_000350.3:c.6089G>A
ClinVar RefSeq Alternation Syntax
NM_001425324.1:c.5867G>A
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2023-06-06
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV004529893
ClinVar Disease
ABCA4-related disorder
Observed Origin Sample
germline
Drugs