Annotation Detail

Information
Associated Genes
FGFR3
Associated Variants
FGFR3 p.Ter809Cysext*? (p.*809Cext*?) ( ENST00000340107.9, ENST00000352904.6, ENST00000412135.7, ENST00000440486.8, ENST00000481110.7 )
FGFR3 p.Ter809Cysext*? (p.*809Cext*?) ( ENST00000340107.9, ENST00000352904.6, ENST00000412135.7, ENST00000440486.8, ENST00000481110.7 )
Associated Disease
FGFR3-related disorder
Source Database
ClinVar
Description
NM_000142.5(FGFR3):c.2421A>T (p.Ter807Cys) AND FGFR3-related disorder
ClinVar Allele ID
31375
ClinVar RefSeq Alternation Syntax
NM_001163213.2:c.2427A>T
ClinVar RefSeq Alternation Syntax
NM_000142.5:c.2421A>T
ClinVar RefSeq Alternation Syntax
NM_001354809.2:c.2424A>T
ClinVar RefSeq Alternation Syntax
NR_148971.2:n.2847A>T
ClinVar RefSeq Alternation Syntax
NM_001354810.2:c.2353A>T
ClinVar RefSeq Alternation Syntax
NM_022965.4:c.2085A>T
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2023-09-09
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV004528117
ClinVar Disease
FGFR3-related disorder
Observed Origin Sample
germline
Drugs