Annotation Detail

Information
Associated Genes
PKD1
Associated Variants
PKD1 p.Arg1672GlyfsTer98 (p.R1672Gfs*98) ( ENST00000262304.9, ENST00000423118.5 )
PKD1 p.Arg1672GlyfsTer98 (p.R1672Gfs*98) ( ENST00000262304.9, ENST00000423118.5 )
Associated Disease
Inborn genetic diseases
Source Database
ClinVar
Description
NM_001009944.3(PKD1):c.5014_5015del (p.Arg1672fs) AND Inborn genetic diseases
ClinVar Allele ID
441862
ClinVar RefSeq Alternation Syntax
NM_000296.4:c.5014_5015del
ClinVar RefSeq Alternation Syntax
NM_001009944.3:c.5014_5015del
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2023-11-14
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV004023518
ClinVar Disease
Inborn genetic diseases
Observed Origin Sample
germline
Drugs