Annotation Detail

Information
Associated Genes
KIT
Associated Variants
KIT p.Val561Asp (p.V561D) ( ENST00000288135.6, ENST00000412167.7, ENST00000686011.1, ENST00000687109.1, ENST00000687246.1, ENST00000687295.1, ENST00000689832.1, ENST00000689994.1, ENST00000690543.1, ENST00000692783.1 )
KIT p.Val561Asp (p.V561D) ( ENST00000288135.6, ENST00000412167.7, ENST00000686011.1, ENST00000687109.1, ENST00000687246.1, ENST00000687295.1, ENST00000689832.1, ENST00000689994.1, ENST00000690543.1, ENST00000692783.1 )
Associated Disease
Hereditary cancer-predisposing syndrome
Source Database
ClinVar
Description
NM_000222.3(KIT):c.1679T>A (p.Val560Asp) AND Hereditary cancer-predisposing syndrome
ClinVar Allele ID
362793
ClinVar RefSeq Alternation Syntax
NM_001385285.1:c.1679T>A
ClinVar RefSeq Alternation Syntax
NM_001385286.1:c.1667T>A
ClinVar RefSeq Alternation Syntax
NM_001385284.1:c.1682T>A
ClinVar RefSeq Alternation Syntax
NM_001385290.1:c.1682T>A
ClinVar RefSeq Alternation Syntax
NM_001385288.1:c.1670T>A
ClinVar RefSeq Alternation Syntax
NM_000222.3:c.1679T>A
ClinVar RefSeq Alternation Syntax
NM_001385292.1:c.1670T>A
ClinVar RefSeq Alternation Syntax
NM_001093772.2:c.1667T>A
Clinical Significance Description
Likely pathogenic
Clinical Significance Last Update
2024-02-23
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV004022196
ClinVar Disease
Hereditary cancer-predisposing syndrome
Observed Origin Sample
germline
Drugs