Annotation Detail

Information
Associated Genes
PSMA6 PRORP-PSMA6
Associated Variants
PSMA6 c.-8C>G, ENSG00000258790 c.*891+13751C>G ( ENST00000627895.2, ENST00000540871.5, ENST00000261479.9, ENST00000555764.5, ENST00000553809.5, ENST00000622405.4, ENST00000628955.1 )
PSMA6 c.-8C>G, ENSG00000258790 c.*891+13751C>G ( ENST00000261479.9, ENST00000540871.5, ENST00000553809.5, ENST00000555764.5, ENST00000622405.4, ENST00000627895.2, ENST00000628955.1 )
Associated Disease
PSMA6-related disorder
Source Database
ClinVar
Description
NM_002791.3(PSMA6):c.-8C>G AND PSMA6-related disorder
ClinVar Allele ID
21835
ClinVar RefSeq Alternation Syntax
NM_001282234.1:c.19+13751C>G
ClinVar RefSeq Alternation Syntax
NM_001282232.1:c.-293C>G
ClinVar RefSeq Alternation Syntax
NM_001282233.1:c.-150C>G
ClinVar RefSeq Alternation Syntax
NM_002791.3:c.-8C>G
ClinVar RefSeq Alternation Syntax
NR_104110.1:n.153C>G
Clinical Significance Description
Benign
Clinical Significance Last Update
2019-10-18
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV003982829
ClinVar Disease
PSMA6-related disorder
Observed Origin Sample
germline
Drugs