Annotation Detail

Information
Associated Genes
HELQ
Associated Variants
HELQ p.Val306Ile (p.V306I) ( ENST00000295488.8, ENST00000510985.1 )
HELQ p.Val306Ile (p.V306I) ( ENST00000295488.8, ENST00000510985.1 )
Associated Disease
HELQ-related disorder
Source Database
ClinVar
Description
NM_133636.5(HELQ):c.916G>A (p.Val306Ile) AND HELQ-related disorder
ClinVar Allele ID
3197404
ClinVar RefSeq Alternation Syntax
NM_001297757.2:c.-619G>A
ClinVar RefSeq Alternation Syntax
NM_001297759.2:c.916G>A
ClinVar RefSeq Alternation Syntax
NM_133636.5:c.916G>A
ClinVar RefSeq Alternation Syntax
NM_001297756.2:c.-589G>A
ClinVar RefSeq Alternation Syntax
NM_001297755.2:c.916G>A
ClinVar RefSeq Alternation Syntax
NR_123737.1:n.1234G>A
ClinVar RefSeq Alternation Syntax
NM_001297758.2:c.805G>A
Clinical Significance Description
Benign
Clinical Significance Last Update
2019-10-17
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV003982500
ClinVar Disease
HELQ-related disorder
Observed Origin Sample
germline
Drugs