Annotation Detail

Information
Associated Genes
PSMA6 PRORP-PSMA6
Associated Variants
PSMA6 c.172-10T>G, ENSG00000258790 c.*987-10T>G ( ENST00000555764.5, ENST00000261479.9, ENST00000553809.5, ENST00000627895.2, ENST00000556506.1, ENST00000540871.5, ENST00000622405.4 )
PSMA6 c.172-10T>G, ENSG00000258790 c.*987-10T>G ( ENST00000261479.9, ENST00000540871.5, ENST00000553809.5, ENST00000555764.5, ENST00000556506.1, ENST00000622405.4, ENST00000627895.2 )
Associated Disease
PSMA6-related disorder
Source Database
ClinVar
Description
NM_002791.3(PSMA6):c.172-10T>G AND PSMA6-related disorder
ClinVar Allele ID
3212732
ClinVar RefSeq Alternation Syntax
NM_001282233.1:c.-66-10T>G
ClinVar RefSeq Alternation Syntax
NM_001282234.1:c.115-10T>G
ClinVar RefSeq Alternation Syntax
NM_002791.3:c.172-10T>G
ClinVar RefSeq Alternation Syntax
NM_001282232.1:c.-66-10T>G
Clinical Significance Description
Likely benign
Clinical Significance Last Update
2019-03-22
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV003954753
ClinVar Disease
PSMA6-related disorder
Observed Origin Sample
germline
Drugs