Annotation Detail

Information
Associated Genes
TGM1
Associated Variants
TGM1 p.Arg286Gln (p.R286Q) ( ENST00000544573.5, ENST00000206765.11 )
TGM1 p.Arg286Gln (p.R286Q) ( ENST00000206765.11, ENST00000544573.5 )
Associated Disease
TGM1-related disorder
Source Database
ClinVar
Description
NM_000359.3(TGM1):c.857G>A (p.Arg286Gln) AND TGM1-related disorder
ClinVar Allele ID
27534
ClinVar RefSeq Alternation Syntax
NM_000359.3:c.857G>A
Clinical Significance Description
Likely pathogenic
Clinical Significance Last Update
2024-02-12
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV003952354
ClinVar Disease
TGM1-related disorder
Observed Origin Sample
germline
Drugs