Annotation Detail

Information
Associated Genes
XPC
Associated Variants
XPC p.Pro334His (p.P334H) ( ENST00000285021.12 )
XPC p.Pro334His (p.P334H) ( ENST00000285021.12 )
Associated Disease
XPC-related disorder
Source Database
ClinVar
Description
NM_004628.5(XPC):c.1001C>A (p.Pro334His) AND XPC-related disorder
ClinVar Allele ID
15292
ClinVar RefSeq Alternation Syntax
NR_148951.2:n.910C>A
ClinVar RefSeq Alternation Syntax
NM_001354726.2:c.422C>A
ClinVar RefSeq Alternation Syntax
NM_004628.5:c.1001C>A
ClinVar RefSeq Alternation Syntax
NM_001354729.2:c.983C>A
ClinVar RefSeq Alternation Syntax
NR_148950.2:n.1034C>A
ClinVar RefSeq Alternation Syntax
NM_001354727.2:c.1001C>A
ClinVar RefSeq Alternation Syntax
NM_001354730.2:c.1001C>A
Clinical Significance Description
Benign
Clinical Significance Last Update
2021-04-10
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV003904788
ClinVar Disease
XPC-related disorder
Observed Origin Sample
germline
Drugs