Annotation Detail

Information
Associated Genes
DYSF
Associated Variants
DYSF p.Asn2051= (p.N2051=) ( ENST00000258104.8, ENST00000394120.6, ENST00000409366.5, ENST00000409582.7, ENST00000409651.5, ENST00000409744.5, ENST00000409762.5, ENST00000410020.8, ENST00000410041.1, ENST00000413539.6, ENST00000429174.6, ENST00000479049.6, ENST00000698058.1, ENST00000698059.1 )
DYSF p.Asn2051= (p.N2051=) ( ENST00000258104.8, ENST00000394120.6, ENST00000409366.5, ENST00000409582.7, ENST00000409651.5, ENST00000409744.5, ENST00000409762.5, ENST00000410020.8, ENST00000410041.1, ENST00000413539.6, ENST00000429174.6, ENST00000479049.6, ENST00000698058.1, ENST00000698059.1 )
Associated Disease
DYSF-related disorder
Source Database
ClinVar
Description
NM_001130987.2(DYSF):c.6153C>T (p.Asn2051=) AND DYSF-related disorder
ClinVar Allele ID
3201406
ClinVar RefSeq Alternation Syntax
NM_001130982.2:c.6132C>T
ClinVar RefSeq Alternation Syntax
NM_001130455.2:c.6039C>T
ClinVar RefSeq Alternation Syntax
NM_001130977.2:c.6057C>T
ClinVar RefSeq Alternation Syntax
NM_001130986.2:c.5997C>T
ClinVar RefSeq Alternation Syntax
NM_001130984.2:c.6060C>T
ClinVar RefSeq Alternation Syntax
NM_001130976.2:c.5994C>T
ClinVar RefSeq Alternation Syntax
NM_003494.4:c.6036C>T
ClinVar RefSeq Alternation Syntax
NM_001130978.2:c.6099C>T
ClinVar RefSeq Alternation Syntax
NM_001130979.2:c.6129C>T
ClinVar RefSeq Alternation Syntax
NM_001130980.2:c.6087C>T
ClinVar RefSeq Alternation Syntax
NM_001130987.2:c.6153C>T
ClinVar RefSeq Alternation Syntax
NM_001130981.2:c.6150C>T
ClinVar RefSeq Alternation Syntax
NM_001130983.2:c.6102C>T
ClinVar RefSeq Alternation Syntax
NM_001130985.2:c.6090C>T
Clinical Significance Description
Likely benign
Clinical Significance Last Update
2021-01-11
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV003897164
ClinVar Disease
DYSF-related disorder
Observed Origin Sample
germline
Drugs