Annotation Detail

Information
Associated Genes
EYS
Associated Variants
EYS p.Cys2350AlafsTer97 (p.C2350Afs*97) ( ENST00000503581.6, ENST00000370621.7 )
EYS p.Cys2350AlafsTer97 (p.C2350Afs*97) ( ENST00000370621.7, ENST00000503581.6 )
Associated Disease
Retinal dystrophy
Source Database
ClinVar
Description
NM_001142800.2(EYS):c.7048del (p.Cys2350fs) AND Retinal dystrophy
ClinVar Allele ID
152827
ClinVar RefSeq Alternation Syntax
NM_001142800.2:c.7048del
ClinVar RefSeq Alternation Syntax
NM_001292009.2:c.7048del
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2023-10-01
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV003888555
ClinVar Disease
Retinal dystrophy
Observed Origin Sample
germline
Drugs