Annotation Detail

Information
Associated Genes
ABCG8
Associated Variants
ABCG8 p.Thr400Met (p.T400M) ( ENST00000272286.4 )
ABCG8 p.Thr400Met (p.T400M) ( ENST00000272286.4 )
Associated Disease
Sitosterolemia 1
Source Database
ClinVar
Description
NM_022437.3(ABCG8):c.1199C>T (p.Thr400Met) AND Sitosterolemia 1
ClinVar Allele ID
2851851
ClinVar RefSeq Alternation Syntax
NM_001357321.2:c.1196C>T
ClinVar RefSeq Alternation Syntax
NM_022437.3:c.1199C>T
Clinical Significance Description
Uncertain significance
Clinical Significance Last Update
2023-07-19
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV003493257
ClinVar Disease
Sitosterolemia 1
Observed Origin Sample
germline
Drugs