Annotation Detail

Information
Associated Genes
OCA2
Associated Variants
OCA2 p.Asn489Asp (p.N489D) ( ENST00000353809.9, ENST00000354638.8 )
OCA2 p.Asn489Asp (p.N489D) ( ENST00000353809.9, ENST00000354638.8 )
Associated Disease
oculocutaneous albinism
Source Database
ClinVar
Description
NM_000275.3(OCA2):c.1465A>G (p.Asn489Asp) AND Oculocutaneous albinism
Observed Origin Sample
germline
ClinVar Allele ID
16000
ClinVar RefSeq Alternation Syntax
NM_001300984.2:c.1393A>G
ClinVar RefSeq Alternation Syntax
NM_000275.3:c.1465A>G
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2023-12-12
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV003492280
ClinVar Disease
Oculocutaneous albinism
Drugs