Annotation Detail

Information
Associated Genes
NF1
Associated Variants
NF1 p.Gln1447Arg (p.Q1447R) ( ENST00000356175.7, ENST00000358273.9, ENST00000691014.1, ENST00000696138.1 )
NF1 p.Gln1447Arg (p.Q1447R) ( ENST00000356175.7, ENST00000358273.9, ENST00000691014.1, ENST00000696138.1 )
Associated Disease
juvenile myelomonocytic leukemia
Source Database
ClinVar
Description
NM_001042492.3(NF1):c.4340A>G (p.Gln1447Arg) AND Juvenile myelomonocytic leukemia
ClinVar Allele ID
186253
ClinVar RefSeq Alternation Syntax
NM_000267.3:c.4277A>G
ClinVar RefSeq Alternation Syntax
NM_001042492.3:c.4340A>G
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2022-11-15
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV003468826
ClinVar Disease
Juvenile myelomonocytic leukemia
Observed Origin Sample
unknown
Drugs