Annotation Detail

Information
Associated Genes
PTEN
Associated Variants
PTEN p.Ile135Val (p.I135V) ( ENST00000371953.8, ENST00000472832.3, ENST00000688308.1, ENST00000700021.1, ENST00000700029.2, ENST00000713839.1 )
PTEN p.Ile135Val (p.I135V) ( ENST00000371953.8, ENST00000472832.3, ENST00000688308.1, ENST00000700021.1, ENST00000700029.2, ENST00000713839.1 )
Associated Disease
Cowden syndrome 1
Source Database
ClinVar
Description
NM_000314.8(PTEN):c.403A>G (p.Ile135Val) AND Cowden syndrome 1
ClinVar Allele ID
152001
ClinVar RefSeq Alternation Syntax
NM_001304718.2:c.-348A>G
ClinVar RefSeq Alternation Syntax
NM_001304717.5:c.922A>G
ClinVar RefSeq Alternation Syntax
NM_000314.8:c.403A>G
Clinical Significance Description
Likely pathogenic
Clinical Significance Last Update
2023-10-20
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV003453083
ClinVar Disease
Cowden syndrome 1
Observed Origin Sample
unknown
Drugs