Annotation Detail

Information
Associated Genes
AIRE
Associated Variants
AIRE p.Leu323SerfsTer51 (p.L323Sfs*51) ( ENST00000291582.6 )
AIRE p.Leu323SerfsTer51 (p.L323Sfs*51) ( ENST00000291582.6 )
Associated Disease
AIRE-related disorder
Source Database
ClinVar
Description
NM_000383.4(AIRE):c.967_979del (p.Leu323fs) AND AIRE-related disorder
ClinVar Allele ID
18348
ClinVar RefSeq Alternation Syntax
NM_000383.4:c.967_979del
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2023-06-15
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV003407265
ClinVar Disease
AIRE-related disorder
Observed Origin Sample
germline
Drugs