Annotation Detail

Information
Associated Genes
OCA2
Associated Variants
OCA2 p.Asn273_Trp274delinsLysVal (p.N273_W274delinsKV) ( ENST00000354638.8, ENST00000353809.9 )
OCA2 p.Asn273_Trp274delinsLysVal (p.N273_W274delinsKV) ( ENST00000353809.9, ENST00000354638.8 )
Associated Disease
OCA2-related disorder
Source Database
ClinVar
Description
NM_000275.3(OCA2):c.819_822delinsGGTC (p.Asn273_Trp274delinsLysVal) AND OCA2-related disorder
ClinVar Allele ID
195868
ClinVar RefSeq Alternation Syntax
NM_001300984.2:c.819_822delinsGGTC
ClinVar RefSeq Alternation Syntax
NM_000275.3:c.819_822delinsGGTC
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2022-12-20
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV003398903
ClinVar Disease
OCA2-related disorder
Observed Origin Sample
germline
Drugs