Annotation Detail

Information
Associated Genes
SOD1
Associated Variants
SOD1 p.Ile114Thr (p.I114T) ( ENST00000270142.11, ENST00000389995.4 )
SOD1 p.Ile114Thr (p.I114T) ( ENST00000270142.11, ENST00000389995.4 )
Associated Disease
SOD1-related disorder
Source Database
ClinVar
Description
NM_000454.5(SOD1):c.341T>C (p.Ile114Thr) AND SOD1-related disorder
ClinVar Allele ID
194306
ClinVar RefSeq Alternation Syntax
NM_000454.5:c.341T>C
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2024-02-16
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV003398894
ClinVar Disease
SOD1-related disorder
Observed Origin Sample
germline
Drugs