Annotation Detail

Information
Associated Genes
SPINK1
Associated Variants
SPINK1 c.194+2T>C ( ENST00000296695.10, ENST00000510027.2 )
SPINK1 c.194+2T>C ( ENST00000296695.10, ENST00000510027.2 )
Associated Disease
SPINK1-related disorder
Source Database
ClinVar
Description
NM_001379610.1(SPINK1):c.194+2T>C AND SPINK1-related disorder
ClinVar Allele ID
136364
ClinVar RefSeq Alternation Syntax
NM_001379610.1:c.194+2T>C
ClinVar RefSeq Alternation Syntax
NM_003122.5:c.194+2T>C
ClinVar RefSeq Alternation Syntax
NM_001354966.2:c.194+2T>C
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2023-08-24
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV003398721
ClinVar Disease
SPINK1-related disorder
Observed Origin Sample
germline
Drugs