Annotation Detail

Information
Associated Genes
GNPTAB
Associated Variants
GNPTAB p.Arg1189Ter (p.R1189*) ( ENST00000299314.12 )
GNPTAB p.Arg1189Ter (p.R1189*) ( ENST00000299314.12 )
Associated Disease
GNPTAB-related disorder
Source Database
ClinVar
Description
NM_024312.5(GNPTAB):c.3565C>T (p.Arg1189Ter) AND GNPTAB-related disorder
ClinVar Allele ID
17803
ClinVar RefSeq Alternation Syntax
NM_024312.5:c.3565C>T
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2023-11-10
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV003398424
ClinVar Disease
GNPTAB-related disorder
Observed Origin Sample
biparental
Drugs