Annotation Detail

Information
Associated Genes
PAH
Associated Variants
PAH p.Ile65Thr (p.I65T) ( ENST00000553106.6, ENST00000307000.7 )
PAH p.Ile65Thr (p.I65T) ( ENST00000307000.7, ENST00000553106.6 )
Associated Disease
PAH-related disorder
Source Database
ClinVar
Description
NM_000277.3(PAH):c.194T>C (p.Ile65Thr) AND PAH-related disorder
ClinVar Allele ID
15675
ClinVar RefSeq Alternation Syntax
NM_001354304.2:c.194T>C
ClinVar RefSeq Alternation Syntax
NM_000277.3:c.194T>C
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2023-08-11
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV003398402
ClinVar Disease
PAH-related disorder
Observed Origin Sample
germline
Drugs