Annotation Detail

Information
Associated Genes
DHCR7
Associated Variants
DHCR7 c.964-1G>C ( ENST00000683287.1, ENST00000355527.8, ENST00000527316.6, ENST00000407721.6, ENST00000526780.6, ENST00000683714.1, ENST00000682708.1, ENST00000685320.1 )
DHCR7 c.964-1G>C ( ENST00000355527.8, ENST00000407721.6, ENST00000526780.6, ENST00000683287.1, ENST00000683714.1, ENST00000685320.1, ENST00000682708.1, ENST00000527316.6 )
Associated Disease
DHCR7-related disorder
Source Database
ClinVar
Description
NM_001360.3(DHCR7):c.964-1G>C AND DHCR7-related disorder
Observed Origin Sample
germline
ClinVar Allele ID
99628
ClinVar RefSeq Alternation Syntax
NM_001360.3:c.964-1G>C
ClinVar RefSeq Alternation Syntax
NM_001163817.2:c.964-1G>C
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2024-02-08
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV003390775
ClinVar Disease
DHCR7-related disorder
Drugs