Annotation Detail

Information
Associated Genes
SOD1 SOD1-DT
Associated Variants
SOD1 p.Ala5Val (p.A5V) ( ENST00000270142.11, ENST00000389995.4 )
SOD1 p.Ala5Val (p.A5V) ( ENST00000270142.11, ENST00000389995.4 )
Associated Disease
SOD1-related disorder
Source Database
ClinVar
Description
NM_000454.5(SOD1):c.14C>T (p.Ala5Val) AND SOD1-related disorder
ClinVar Allele ID
29802
ClinVar RefSeq Alternation Syntax
NM_000454.5:c.14C>T
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2023-09-12
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV003390686
ClinVar Disease
SOD1-related disorder
Observed Origin Sample
germline
Drugs