Annotation Detail

Information
Associated Genes
KCNJ11
Associated Variants
KCNJ11 p.Arg50Gln (p.R50Q) ( ENST00000339994.5, ENST00000682350.1, ENST00000682764.1, ENST00000528731.1 )
KCNJ11 p.Arg50Gln (p.R50Q) ( ENST00000339994.5, ENST00000528731.1, ENST00000682350.1, ENST00000682764.1 )
Associated Disease
Diabetes mellitus, permanent neonatal 2
Source Database
ClinVar
Description
NM_000525.4(KCNJ11):c.149G>A (p.Arg50Gln) AND Diabetes mellitus, permanent neonatal 2
ClinVar Allele ID
45094
ClinVar RefSeq Alternation Syntax
NM_001377297.1:c.-16-97G>A
ClinVar RefSeq Alternation Syntax
NM_000525.4:c.149G>A
ClinVar RefSeq Alternation Syntax
NM_001166290.2:c.-16-97G>A
ClinVar RefSeq Alternation Syntax
NM_001377296.1:c.-17+75G>A
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2023-10-30
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV003387732
ClinVar Disease
Diabetes mellitus, permanent neonatal 2
Observed Origin Sample
germline
Drugs