Annotation Detail

Information
Associated Genes
COL7A1
Associated Variants
COL7A1 p.Gly2749Ter (p.G2749*) ( ENST00000328333.12, ENST00000681320.1 )
COL7A1 p.Gly2749Ter (p.G2749*) ( ENST00000328333.12, ENST00000681320.1 )
Associated Disease
recessive dystrophic epidermolysis bullosa
Source Database
ClinVar
Description
NM_000094.4(COL7A1):c.8245G>T (p.Gly2749Ter) AND Recessive dystrophic epidermolysis bullosa
ClinVar Allele ID
2744756
ClinVar RefSeq Alternation Syntax
NM_000094.4:c.8245G>T
Clinical Significance Description
Likely pathogenic
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV003328130
ClinVar Disease
Recessive dystrophic epidermolysis bullosa
Observed Origin Sample
germline
Drugs