Annotation Detail

Information
Associated Genes
TGM1
Associated Variants
TGM1 p.Asp490Gly (p.D490G) ( ENST00000544573.5, ENST00000206765.11 )
TGM1 p.Asp490Gly (p.D490G) ( ENST00000206765.11, ENST00000544573.5 )
Associated Disease
Lamellar ichthyosis
Source Database
ClinVar
Description
NM_000359.3(TGM1):c.1469A>G (p.Asp490Gly) AND Lamellar ichthyosis
ClinVar Allele ID
27530
ClinVar RefSeq Alternation Syntax
NM_000359.3:c.1469A>G
Clinical Significance Description
Likely pathogenic
Clinical Significance Last Update
2023-03-03
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV003226158
ClinVar Disease
Lamellar ichthyosis
Observed Origin Sample
germline
Drugs