Annotation Detail

Information
Associated Genes
TTC7A
Associated Variants
TTC7A p.Cys299Ser (p.C299S) ( ENST00000319190.11, ENST00000394850.6, ENST00000409245.5 )
TTC7A p.Cys299Ser (p.C299S) ( ENST00000319190.11, ENST00000394850.6, ENST00000409245.5 )
Associated Disease
Gastrointestinal defects and immunodeficiency syndrome 1
Source Database
ClinVar
Description
NM_020458.4(TTC7A):c.895T>A (p.Cys299Ser) AND Gastrointestinal defects and immunodeficiency syndrome 1
ClinVar Allele ID
980447
ClinVar RefSeq Alternation Syntax
NM_020458.4:c.895T>A
ClinVar RefSeq Alternation Syntax
NM_001288955.2:c.-61-728T>A
ClinVar RefSeq Alternation Syntax
NM_001288953.2:c.793T>A
ClinVar RefSeq Alternation Syntax
NM_001288951.2:c.895T>A
Clinical Significance Description
Uncertain significance
Clinical Significance Last Update
2021-03-30
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV003224540
ClinVar Disease
Gastrointestinal defects and immunodeficiency syndrome 1
Observed Origin Sample
germline
Drugs