Annotation Detail

Information
Associated Genes
TPM3
Associated Variants
TPM3 p.Met9Arg (p.M9R) ( ENST00000651641.1, ENST00000368530.7, ENST00000271850.11 )
TPM3 p.Met9Arg (p.M9R) ( ENST00000271850.11, ENST00000368530.7, ENST00000651641.1 )
Associated Disease
Congenital myopathy 4A, autosomal dominant
Source Database
ClinVar
Description
NM_152263.4(TPM3):c.26T>G (p.Met9Arg) AND Congenital myopathy 4A, autosomal dominant
ClinVar Allele ID
27485
ClinVar RefSeq Alternation Syntax
NR_103460.2:n.108T>G
ClinVar RefSeq Alternation Syntax
NM_001364679.2:c.26T>G
ClinVar RefSeq Alternation Syntax
NM_152263.4:c.26T>G
ClinVar RefSeq Alternation Syntax
NM_001364681.2:c.26T>G
ClinVar RefSeq Alternation Syntax
NM_001364682.1:c.26T>G
ClinVar RefSeq Alternation Syntax
NM_001364680.2:c.26T>G
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2005-01-01
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV003151723
ClinVar Disease
Congenital myopathy 4A, autosomal dominant
Observed Origin Sample
germline
Pubmed
10587521
Pubmed
7704029
Pubmed
15562513
Drugs