Annotation Detail

Information
Associated Genes
PNKD CATIP-AS2
Associated Variants
PNKD p.Arg368Trp (p.R368W) ( ENST00000273077.9, ENST00000258362.7, ENST00000436005.3, ENST00000685415.1, ENST00000687736.1, ENST00000688179.1, ENST00000689816.1, ENST00000691220.1, ENST00000692295.1 )
PNKD p.Arg368Trp (p.R368W) ( ENST00000258362.7, ENST00000273077.9, ENST00000436005.3, ENST00000685415.1, ENST00000687736.1, ENST00000688179.1, ENST00000689816.1, ENST00000691220.1, ENST00000692295.1 )
Associated Disease
paroxysmal nonkinesigenic dyskinesia 1
Source Database
ClinVar
Description
NM_015488.5(PNKD):c.1102C>T (p.Arg368Trp) AND Paroxysmal nonkinesigenic dyskinesia 1
ClinVar Allele ID
1133184
ClinVar RefSeq Alternation Syntax
NM_015488.5:c.1102C>T
ClinVar RefSeq Alternation Syntax
NM_022572.4:c.1030C>T
Clinical Significance Description
Uncertain significance
Clinical Significance Last Update
2023-02-02
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV003130528
ClinVar Disease
Paroxysmal nonkinesigenic dyskinesia 1
Observed Origin Sample
germline
Drugs