Annotation Detail

Information
Associated Genes
MEFV
Associated Variants
MEFV p.Pro369Thr (p.P369T) ( ENST00000536379.5, ENST00000219596.6, ENST00000339854.8, ENST00000541159.5 )
MEFV p.Pro369Thr (p.P369T) ( ENST00000219596.6, ENST00000339854.8, ENST00000536379.5, ENST00000541159.5 )
Associated Disease
Acute febrile neutrophilic dermatosis
Source Database
ClinVar
Description
NM_000243.3(MEFV):c.1105C>A (p.Pro369Thr) AND Acute febrile neutrophilic dermatosis
ClinVar Allele ID
875213
ClinVar RefSeq Alternation Syntax
NM_001198536.2:c.472C>A
ClinVar RefSeq Alternation Syntax
NM_000243.3:c.1105C>A
Clinical Significance Description
Likely benign
Clinical Significance Last Update
2023-02-08
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV003127638
ClinVar Disease
Acute febrile neutrophilic dermatosis
Observed Origin Sample
germline
Drugs